Figure 2.
The table is divided into several sections: Baseline Assessment, Skin, Pulmonary, Vascular, Lymphoproliferation, Musculoskeletal, and Dental. Each section lists specific assessments and management strategies. The Baseline Assessment section includes tests like full blood count, pulmonary function tests, and cross-sectional chest imaging. The Skin section covers baseline management guidelines for atopic dermatitis, including topical treatments and surgical management. The Pulmonary section outlines follow-up imaging, spirometry, and regular exercise. The Vascular section includes individualized CT/MR angiography and regular cardiovascular monitoring. The Lymphoproliferation section details annual clinical evaluations and symptom-driven imaging. The Musculoskeletal section focuses on patient education, treatment of scoliosis, and lifestyle measures. The Dental section emphasizes the removal of retained primary teeth and collaboration with experienced dentists. The table also includes a section on the age of onset for manifestations, divided into three age ranges: 0-10 years, 10-30 years, and 30+ years, listing characteristic features and risks associated with each age range.
Organ-specific manifestations of STAT3-HIES.