Hematological and immunological findings of the proband over time
| Parameter (units) | Age (years) | 13.96 | 14.08 | 14.2 | 14.45 | 14.78 | 14.98 | 15.16 | 15.54 |
|---|---|---|---|---|---|---|---|---|---|
| Normal range | Pre-tofacitinib | Post-tofacitinib | |||||||
| Hemoglobin (g/L) | 130–180 | 108 | 109 | 112 | 114 | 115 | 130 | 124 | 119 |
| Ferritin (µg/L) | 20–340 | 63 | N/A | N/A | N/A | 25 | N/A | 24 | N/A |
| Mean corpuscular volume (fl) | 78–98 | 80 | 81 | 81 | 82 | 83 | 82 | 80 | 81 |
| Total leukocytes (×109/L) | 4–11 | 5.8 | 5.7 | 5.5 | 5.5 | 6 | 4.1 | 4.1 | 5.5 |
| Total lymphocytes (×109/L) | 1–4 | 2.5 | 2.8 | 3 | 3 | 3.5 | 2.9 | 2.3 | 2.6 |
| CD19+ B cells (×106/L) | 110–570 | 640 | 836 | 1,029 | 1,257 | 1,319 | N/A | N/A | 895 |
| Switched memory B cells* (106/L) | 30–110 | N/A | N/A | 7 | N/A | N/A | N/A | N/A | 25 |
| NK cells** (×106/L) | 70–480 | 27 | 34 | 41 | 44 | 125 | N/A | N/A | 88 |
| Neutrophils (×109/L) | 2–8 | 2.8 | 2.4 | 2 | 1.9 | 2 | 0.94 | 1.4 | 2.3 |
| Platelets (×109/L) | 150–450 | 506 | 502 | 496 | 461 | 514 | 437 | 406 | 455 |
| Immunoglobulin G (g/L) | 6.6–15.3 | 21.5 | 24.4 | N/A | 21.9 | 19.9 | N/A | N/A | 23.2 |
| C-reactive protein (mg/L) | 0–5 | 0.4 | N/A | <0.2 | <0.2 | <0.2 | <0.2 | N/A | <0.2 |
| ESR (mm/h) | 0–10 | 22 | N/A | 15 | 8 | 11 | 9 | 9 | 20 |
| Serum amyloid A (mg/L) | 0.0–6.4 | N/A | N/A | <4 | N/A | N/A | N/A | N/A | N/A |
| Parameter (units) | Age (years) | 13.96 | 14.08 | 14.2 | 14.45 | 14.78 | 14.98 | 15.16 | 15.54 |
|---|---|---|---|---|---|---|---|---|---|
| Normal range | Pre-tofacitinib | Post-tofacitinib | |||||||
| Hemoglobin (g/L) | 130–180 | 130 | |||||||
| Ferritin (µg/L) | 20–340 | 63 | N/A | N/A | N/A | 25 | N/A | 24 | N/A |
| Mean corpuscular volume (fl) | 78–98 | 80 | 81 | 81 | 82 | 83 | 82 | 80 | 81 |
| Total leukocytes (×109/L) | 4–11 | 5.8 | 5.7 | 5.5 | 5.5 | 6 | 4.1 | 4.1 | 5.5 |
| Total lymphocytes (×109/L) | 1–4 | 2.5 | 2.8 | 3 | 3 | 3.5 | 2.9 | 2.3 | 2.6 |
| CD19+ B cells (×106/L) | 110–570 | N/A | N/A | ||||||
| Switched memory B cells* (106/L) | 30–110 | N/A | N/A | N/A | N/A | N/A | N/A | ||
| NK cells** (×106/L) | 70–480 | 125 | N/A | N/A | 88 | ||||
| Neutrophils (×109/L) | 2–8 | 2.8 | 2.4 | 2 | 2 | 2.3 | |||
| Platelets (×109/L) | 150–450 | 437 | 406 | ||||||
| Immunoglobulin G (g/L) | 6.6–15.3 | N/A | N/A | N/A | |||||
| C-reactive protein (mg/L) | 0–5 | 0.4 | N/A | <0.2 | <0.2 | <0.2 | <0.2 | N/A | <0.2 |
| ESR (mm/h) | 0–10 | N/A | 8 | 9 | 9 | ||||
| Serum amyloid A (mg/L) | 0.0–6.4 | N/A | N/A | <4 | N/A | N/A | N/A | N/A | N/A |
N/A, not assessed; italic denotes above normal range, and bold denotes below normal range. *CD19+/CD27+/IgM−/IgD−; **CD3−/CD16+/CD56+.
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