Table 1.

Demographic characteristics of efficacy outcome cohort

Cohort (n = 97)
Sex, n (%) ​ 
Male 58 (60) 
Race, n (%) ​ 
White 68 (70) 
Black, African American 21 (22) 
Asian 3 (3) 
American Indian 2 (2) 
Native Hawaiian 1 (1) 
>1 race 2 (2) 
Ethnicity, n (%) ​ 
Hispanic or Latino 18 (19) 
Not Hispanic or Latino 79 (81) 
Genetic/syndromic etiology, n (%) ​ 
22q11.2 deletion 36 (37) 
CHARGE/CHD7 mutationa 24 (25) 
FOXN1 mutation 2 (2) 
PAX1 mutation 1 (1) 
TBX2 mutation 1 (1) 
Diabetic embryopathy 21 (22) 
No known mutation/syndrome 12 (12) 
Syndromic comorbidities, n (%) ​ 
Choanal atresia 11 (11) 
Cleft palate or submucous cleft 17 (17) 
Coloboma 19 (20) 
Congenital cardiac anomaly 87 (90) 
Deafness or ear pinnae anomalies 50 (51) 
Dysmorphic facies 45 (46) 
Tracheal anomalies 25 (26) 
Genital hypoplasia 12 (12) 
Hypocalcemia 82 (84) 
Anal/rectal anomalies 6 (6) 
Renal anomalies 26 (27) 
Autoimmunity, n (%) ​ 
Rashb 37 (38) 
Symptomatic GVHDc 2 (2) 
Thrombocytopenia 10 (10) 
Neutropenia 6 (6) 
Autoimmune hemolytic anemia 6 (6) 
Hypothyroid 6 (6) 
Age at time of implantation (months) ​ 
Median (Q1; Q3) 9 (4; 14) 
Minimum, maximum 1, 53 
a

CHARGE/CHD7 numbers are based on phenotype or genetic testing.

b

Based on skin biopsy.

c

Due to maternal T cells or nonirradiated blood transfusion.

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