XLA SGRQ scores (median, IQR) compared those with and without bronchiectasis and against UK healthy norms (mean, 95% CI) (32) and UK CF patients (mean, SD) (33)
| . | UK XLA patients (n = 43) . | UK norms . | P value . | CF patients . | P value . |
|---|---|---|---|---|---|
| Symptom score | 43.41 (14.32, 58.58) | 12 (9–15) | <0.001 | 35.29 (19.3) | 0.267 |
| Activity score | 18.47 (4.48, 35.61) | 9 (7–12) | <0.001 | 28.90 (25.2) | 0.412 |
| Impact score | 14.58 (4.58, 24.23) | 2 (1–3) | <0.001 | 18.60 (14.6) | 0.246 |
| Total score | 21.06 (6.37 – 27.86) | 6 (5–7) | <0.001 | 24.50 (16.8) | 0.156 |
| . | UK XLA patients (n = 43) . | UK norms . | P value . | CF patients . | P value . |
|---|---|---|---|---|---|
| Symptom score | 43.41 (14.32, 58.58) | 12 (9–15) | <0.001 | 35.29 (19.3) | 0.267 |
| Activity score | 18.47 (4.48, 35.61) | 9 (7–12) | <0.001 | 28.90 (25.2) | 0.412 |
| Impact score | 14.58 (4.58, 24.23) | 2 (1–3) | <0.001 | 18.60 (14.6) | 0.246 |
| Total score | 21.06 (6.37 – 27.86) | 6 (5–7) | <0.001 | 24.50 (16.8) | 0.156 |
| . | Bronchiectasis . | No bronchiectasis . | P value . | Bronchiectasis versus male UK norms . | Bronchiectasis versus CF patients . |
|---|---|---|---|---|---|
| Symptom score | 56.33 (38.44, 68.26) | 11.89 (0.00, 19.03) | <0.001 | <0.001 | 0.001 |
| Activity score | 30.81 (18.47, 43.48) | 1.16 (0.00, 5.96) | <0.001 | <0.001 | 0.517 |
| Impact score | 21.66 (14.50, 31.39) | 1.89 (0.00, 5.52) | <0.001 | <0.001 | 0.139 |
| Total score | 26.84 (21.05, 32.94) | 4.81 (1.52, 8.63) | <0.001 | <0.001 | 0.198 |
| . | Bronchiectasis . | No bronchiectasis . | P value . | Bronchiectasis versus male UK norms . | Bronchiectasis versus CF patients . |
|---|---|---|---|---|---|
| Symptom score | 56.33 (38.44, 68.26) | 11.89 (0.00, 19.03) | <0.001 | <0.001 | 0.001 |
| Activity score | 30.81 (18.47, 43.48) | 1.16 (0.00, 5.96) | <0.001 | <0.001 | 0.517 |
| Impact score | 21.66 (14.50, 31.39) | 1.89 (0.00, 5.52) | <0.001 | <0.001 | 0.139 |
| Total score | 26.84 (21.05, 32.94) | 4.81 (1.52, 8.63) | <0.001 | <0.001 | 0.198 |
Values in italics are those that are statistically significant (P <0.05).