SF36v2 physical health scores for the cohort and by presence of bronchiectasis (median, IQR) compared to male UK norms (30) and UK male patients with CF (31) (mean, SD)
| . | UK XLA patients (n = 42) . | UK norms . | P value . | CF patients . | P value . |
|---|---|---|---|---|---|
| Physical function | 95.00 (90.00, 100.00) | 89.76 (18.78) | 0.062 | 82.4 (20.7) | 0.010 |
| Role—physical | 96.88 (87.50, 100.00) | 89.01 (21.09) | 0.083 | 75.00 (22.5) | 0.004 |
| Pain | 74.00 (62.00, 100.00) | 81.25 (22.21) | 0.335 | 84.2 (19.6) | 0.249 |
| General health | 37.00 (22.00, 52.00) | 70.86 (20.29) | <0.001 | 46.8 (24.0) | 0.077 |
| PCS | 49.10 (47.14, 54.95) | 50.63 (9.41) | 0.712 | N/A | N/A |
| . | UK XLA patients (n = 42) . | UK norms . | P value . | CF patients . | P value . |
|---|---|---|---|---|---|
| Physical function | 95.00 (90.00, 100.00) | 89.76 (18.78) | 0.062 | 82.4 (20.7) | 0.010 |
| Role—physical | 96.88 (87.50, 100.00) | 89.01 (21.09) | 0.083 | 75.00 (22.5) | 0.004 |
| Pain | 74.00 (62.00, 100.00) | 81.25 (22.21) | 0.335 | 84.2 (19.6) | 0.249 |
| General health | 37.00 (22.00, 52.00) | 70.86 (20.29) | <0.001 | 46.8 (24.0) | 0.077 |
| PCS | 49.10 (47.14, 54.95) | 50.63 (9.41) | 0.712 | N/A | N/A |
| . | Bronchiectasis . | No bronchiectasis . | Bronchiectasis versus no bronchiectasis . | Bronchiectasis versus male UK norms . | Bronchiectasis versus CF patients . |
|---|---|---|---|---|---|
| Physical function | 90.0 (85.00, 95.00) | 100.00 (100.00, 100.00) | <0.001 | 0.515 | 0.311 |
| Role—physical | 93.75 (75.00, 100.00) | 100.00 (100.00, 100.00) | 0.008 | 0.923 | 0.260 |
| Pain | 74.00 (62.00, 84.00) | 100.00 (100.00, 100.00) | <0.001 | 0.005 | 0.003 |
| General health | 25.00 (17.00, 37.00) | 57.00 (52.00, 75.00) | <0.001 | <0.001 | 0.001 |
| PCS | 47.88 (44.94, 50.09) | 55.14 (53.30, 57.47) | <0.001 | 0.004 | N/A |
| . | Bronchiectasis . | No bronchiectasis . | Bronchiectasis versus no bronchiectasis . | Bronchiectasis versus male UK norms . | Bronchiectasis versus CF patients . |
|---|---|---|---|---|---|
| Physical function | 90.0 (85.00, 95.00) | 100.00 (100.00, 100.00) | <0.001 | 0.515 | 0.311 |
| Role—physical | 93.75 (75.00, 100.00) | 100.00 (100.00, 100.00) | 0.008 | 0.923 | 0.260 |
| Pain | 74.00 (62.00, 84.00) | 100.00 (100.00, 100.00) | <0.001 | 0.005 | 0.003 |
| General health | 25.00 (17.00, 37.00) | 57.00 (52.00, 75.00) | <0.001 | <0.001 | 0.001 |
| PCS | 47.88 (44.94, 50.09) | 55.14 (53.30, 57.47) | <0.001 | 0.004 | N/A |
Values in italics are those that are statistically significant (P <0.05).