Table 1.

Patient demographics and transplant characteristics

Patient demographicNo. (%)
Sex 
Male 35 (83.3%) 
Female 7 (16.7%) 
Median age in years at first HSCT (range) 6 (0.9–15.2 years) 
Median age in years at last follow-up (range) 16.8 (6.0–22.0 years) 
Median follow-up time post first HSCT in years (range) 8 (2.4–13.8 years) 
CGD diagnosis 42 
XL-CGD 29 (69.0%) 
p47 8 (19.0%) 
p67 3 (7.1%) 
p22 2 (4.8%) 
Number of interventions 45 
One HSCT 42 (93.3%) 
Post-HSCT DLI 3 (6.6%) 
DLI followed by second HSCT 2 (4.4%) 
Post-HSCT gene therapy 1 (2.2%) 
Donor 45 
MUD 23 (51.1%) 
MSD 11 (24.4%) 
MMUD 10 (22.2%) 
MFD 1 (2.2%) 
Conditioning intensity 45 
Myeloablative (MAC) 11 (24.4%) 
—Bu/Cy 6 (13.3%) 
—Bu/Flu 3 (6.7%
—Treo/Thio/Flu 2 (4.4%) 
Reduced intensity (RIC) 34 (75.6%) 
—Flu/Bu 20 (44.4%) 
—Flu/Treo 12 (26.7%) 
—Flu/Melph 1 (2.2%) 
—Bu/Cy 1 (2.2%) 
Transplant cells 45 
Bone marrow 25 (55.5%) 
PBSC 18 (40.0%) 
Cord 2 (4.4%) 
GvHD prophylaxis 45 
CSA + MMF 35 (77.8%) 
CSA + MTX 6 (13.3%) 
CSA + Methylprednisolone 1 (2.2%) 
CSA only 2 (4.4%) 
None 1 (2.2%) 
Patient demographicNo. (%)
Sex 
Male 35 (83.3%) 
Female 7 (16.7%) 
Median age in years at first HSCT (range) 6 (0.9–15.2 years) 
Median age in years at last follow-up (range) 16.8 (6.0–22.0 years) 
Median follow-up time post first HSCT in years (range) 8 (2.4–13.8 years) 
CGD diagnosis 42 
XL-CGD 29 (69.0%) 
p47 8 (19.0%) 
p67 3 (7.1%) 
p22 2 (4.8%) 
Number of interventions 45 
One HSCT 42 (93.3%) 
Post-HSCT DLI 3 (6.6%) 
DLI followed by second HSCT 2 (4.4%) 
Post-HSCT gene therapy 1 (2.2%) 
Donor 45 
MUD 23 (51.1%) 
MSD 11 (24.4%) 
MMUD 10 (22.2%) 
MFD 1 (2.2%) 
Conditioning intensity 45 
Myeloablative (MAC) 11 (24.4%) 
—Bu/Cy 6 (13.3%) 
—Bu/Flu 3 (6.7%
—Treo/Thio/Flu 2 (4.4%) 
Reduced intensity (RIC) 34 (75.6%) 
—Flu/Bu 20 (44.4%) 
—Flu/Treo 12 (26.7%) 
—Flu/Melph 1 (2.2%) 
—Bu/Cy 1 (2.2%) 
Transplant cells 45 
Bone marrow 25 (55.5%) 
PBSC 18 (40.0%) 
Cord 2 (4.4%) 
GvHD prophylaxis 45 
CSA + MMF 35 (77.8%) 
CSA + MTX 6 (13.3%) 
CSA + Methylprednisolone 1 (2.2%) 
CSA only 2 (4.4%) 
None 1 (2.2%) 

Patients (n = 42) and transplants (n = 45). Bu, busulfan; CSA, ciclosporin; Cy, cyclophosphamide; Flu, fludarabine; Melph, melphalan; MFD, matched family donor; MMF, mycophenolate; MTX, methotrexate; PBSC, peripheral blood stem cell; Thio, thiotepa; Treo, treosulfan.

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