Table 1.

Clinical information on MIS-A patients

MIS-A 1MIS-A 2MIS-A 3MIS-A 4MIS-A 5
Age 33 50 23 38 35 
Gender Male Male Female Female Female 
Time from verified SARS-CoV-2 infection to admission 7 wk 3 wk 6 wk 0 day 3 wk 
Symptoms from MIS-A period Persistent fever, dry cough, dyspnea, abdominal discomfort, diarrhea, respiratory and circulatory failure, and universal rash resembling erythema multiforme Persistent fever, headache, sore throat, aching muscles and joints, abdominal pain, swollen lymph node on left side of neck, universal rash, and respiratory distress High fever, myalgia, throat irritation, cough, expectoration, retrosternal chest pain, conjunctival injection, chapped lips, and bilateral lung consolidation Persistent fever, sore throat, diarrhea, hypotension (80/60 mmHg), and myocarditis High fever, abdominal pain, vomiting, myalgia (especially in lower extremities), labile blood pressure, and multiorgan failure 
Treatment IVIG, hydrocortisone, fluid resuscitation, vasopressor therapy, hemodialysis, ceftriaxone, clarithromycin, and respirator IVIG, hydrocortisone, fluid resuscitation, Pip/Tazo, meropenem, clindamycin, and metronidazole IVIG, methylprednisolone, acetylsalicylic acid, penicillin, and ciprofloxacin IVIG, fluid resuscitation, and Pip/Tazo Pip/Tazo and clindamycin 
Time of blood sampling after first symptoms 2 days 14 days 21 days 5 days 11 days 
Treatment before blood sampling Yes, during sampling Yes, just prior to sampling Yes, just prior to sampling Yes, during sampling Yes, just prior to sampling 
COVID-19 vaccination status prior to MIS-A No No No No Yes, vaccinated × 2 (before MIS period) 
MIS-A 1MIS-A 2MIS-A 3MIS-A 4MIS-A 5
Age 33 50 23 38 35 
Gender Male Male Female Female Female 
Time from verified SARS-CoV-2 infection to admission 7 wk 3 wk 6 wk 0 day 3 wk 
Symptoms from MIS-A period Persistent fever, dry cough, dyspnea, abdominal discomfort, diarrhea, respiratory and circulatory failure, and universal rash resembling erythema multiforme Persistent fever, headache, sore throat, aching muscles and joints, abdominal pain, swollen lymph node on left side of neck, universal rash, and respiratory distress High fever, myalgia, throat irritation, cough, expectoration, retrosternal chest pain, conjunctival injection, chapped lips, and bilateral lung consolidation Persistent fever, sore throat, diarrhea, hypotension (80/60 mmHg), and myocarditis High fever, abdominal pain, vomiting, myalgia (especially in lower extremities), labile blood pressure, and multiorgan failure 
Treatment IVIG, hydrocortisone, fluid resuscitation, vasopressor therapy, hemodialysis, ceftriaxone, clarithromycin, and respirator IVIG, hydrocortisone, fluid resuscitation, Pip/Tazo, meropenem, clindamycin, and metronidazole IVIG, methylprednisolone, acetylsalicylic acid, penicillin, and ciprofloxacin IVIG, fluid resuscitation, and Pip/Tazo Pip/Tazo and clindamycin 
Time of blood sampling after first symptoms 2 days 14 days 21 days 5 days 11 days 
Treatment before blood sampling Yes, during sampling Yes, just prior to sampling Yes, just prior to sampling Yes, during sampling Yes, just prior to sampling 
COVID-19 vaccination status prior to MIS-A No No No No Yes, vaccinated × 2 (before MIS period) 
MIS-A 6MIS-A 7MIS-A 8MIS-A 9MIS-A 10
Age 46 32 39 18 44 
Gender Male Male Female Male Male 
Time from verified SARS-CoV-2 infection to admission 7 wk 5 wk Unknown 5 wk 6 wk 
Symptoms from MIS-A period Fever, headache, adenomegaly, dysarthria, confusion, and refractory cardiogenic shock Chest pain, syncope, complete heart block, and cardiogenic shock Dyspnea and mixed distributive and cardiogenic shock Fever, abdominal discomfort, diarrhea, universal rash, chest pain, and cardiogenic shock Fever, diarrhea, abdominal pain, and cardiogenic shock 
Treatment Fluid therapy,
vasopressor,
inotropes, VA-ECMO,
methylprednisolone,
IVIG 
External cardiac pacing,
inotropes,
methylprednisolone,
IVIG 
Fluid therapy,
vasopressors,
mechanical, ventilation
renal replacement therapy, VA-ECMO,
methylprednisolone,
IVIG 
Inotropes, VA-ECMO,
methylprednisolone,
IVIG 
Fluid therapy,
inotropes,
vasopressors,
mechanical ventilation,
VA-ECMO,
renal replacement therapy,
methylprednisolone,
IVIG 
Time of blood sampling after first symptoms 5 days 6 days 12 days 7 days 1 day 
Treatment before blood sampling Yes, just prior to sampling Yes, just prior to sampling Yes, just prior to sampling Yes, just prior to sampling No 
COVID-19 vaccination status prior to MIS-A Yes, 3 doses (last dose 10 mo prior) Unknown Yes, 2 doses Unknown No 
MIS-A 6MIS-A 7MIS-A 8MIS-A 9MIS-A 10
Age 46 32 39 18 44 
Gender Male Male Female Male Male 
Time from verified SARS-CoV-2 infection to admission 7 wk 5 wk Unknown 5 wk 6 wk 
Symptoms from MIS-A period Fever, headache, adenomegaly, dysarthria, confusion, and refractory cardiogenic shock Chest pain, syncope, complete heart block, and cardiogenic shock Dyspnea and mixed distributive and cardiogenic shock Fever, abdominal discomfort, diarrhea, universal rash, chest pain, and cardiogenic shock Fever, diarrhea, abdominal pain, and cardiogenic shock 
Treatment Fluid therapy,
vasopressor,
inotropes, VA-ECMO,
methylprednisolone,
IVIG 
External cardiac pacing,
inotropes,
methylprednisolone,
IVIG 
Fluid therapy,
vasopressors,
mechanical, ventilation
renal replacement therapy, VA-ECMO,
methylprednisolone,
IVIG 
Inotropes, VA-ECMO,
methylprednisolone,
IVIG 
Fluid therapy,
inotropes,
vasopressors,
mechanical ventilation,
VA-ECMO,
renal replacement therapy,
methylprednisolone,
IVIG 
Time of blood sampling after first symptoms 5 days 6 days 12 days 7 days 1 day 
Treatment before blood sampling Yes, just prior to sampling Yes, just prior to sampling Yes, just prior to sampling Yes, just prior to sampling No 
COVID-19 vaccination status prior to MIS-A Yes, 3 doses (last dose 10 mo prior) Unknown Yes, 2 doses Unknown No 
MIS-A 11MIS-A 12MIS-A 13MIS-A 14MIS-A 15
Age 22 33 25 25 19 
Gender Female Male Male Female Male 
Time from verified SARS-CoV-2 infection to admission 3 wk 4 wk 7 days Unknown 4 wk 
Symptoms from MIS-A period Fever, cough, sore throat, headache, diarrhea, conjunctivitis, and cardiogenic shock Fever, adenomegaly, sore throat, and cardiogenic shock Sore throat, fever, and myocarditis Fever, sore throat, chest pain, and cardiogenic shock Diarrhea, myalgia, dyspnea, and cardiogenic shock 
Treatment Fluid therapy,
inotropes,
vasopressors,
methylprednisolone,
IVIG 
Fluid therapy,
inotropes,
vasopressors,
methylprednisolone,
IVIG 
Inotropes,
methylprednisolone,
IVIG 
Inotropes,
vasopressors,
VA-ECMO,
methylprednisolone,
IVIG 
Inotropes,
vasopressors,
VA-ECMO,
methylprednisolone,
IVIG 
Time of blood sampling after first symptoms 9 days 3 days 7 days 3 days 5 days 
Treatment before blood sampling Yes, just prior to sampling Yes, just prior to sampling Yes, just prior to sampling No Yes, just prior to sampling 
COVID-19 vaccination status prior to MIS-A No Unknown No No No 
MIS-A 11MIS-A 12MIS-A 13MIS-A 14MIS-A 15
Age 22 33 25 25 19 
Gender Female Male Male Female Male 
Time from verified SARS-CoV-2 infection to admission 3 wk 4 wk 7 days Unknown 4 wk 
Symptoms from MIS-A period Fever, cough, sore throat, headache, diarrhea, conjunctivitis, and cardiogenic shock Fever, adenomegaly, sore throat, and cardiogenic shock Sore throat, fever, and myocarditis Fever, sore throat, chest pain, and cardiogenic shock Diarrhea, myalgia, dyspnea, and cardiogenic shock 
Treatment Fluid therapy,
inotropes,
vasopressors,
methylprednisolone,
IVIG 
Fluid therapy,
inotropes,
vasopressors,
methylprednisolone,
IVIG 
Inotropes,
methylprednisolone,
IVIG 
Inotropes,
vasopressors,
VA-ECMO,
methylprednisolone,
IVIG 
Inotropes,
vasopressors,
VA-ECMO,
methylprednisolone,
IVIG 
Time of blood sampling after first symptoms 9 days 3 days 7 days 3 days 5 days 
Treatment before blood sampling Yes, just prior to sampling Yes, just prior to sampling Yes, just prior to sampling No Yes, just prior to sampling 
COVID-19 vaccination status prior to MIS-A No Unknown No No No 
MIS-A 16
Age 16 
Gender Male 
Time from verified SARS-CoV-2 infection to admission Unknown 
Symptoms from MIS-A period Chest pain, headache, fever, abdominal discomfort, and cardiogenic shock 
Treatment Inotropes, methylprednisolone 
Time of blood sampling after first symptoms 2 days 
Treatment before blood sampling No 
COVID-19 vaccination status prior to MIS-A Unknown 
MIS-A 16
Age 16 
Gender Male 
Time from verified SARS-CoV-2 infection to admission Unknown 
Symptoms from MIS-A period Chest pain, headache, fever, abdominal discomfort, and cardiogenic shock 
Treatment Inotropes, methylprednisolone 
Time of blood sampling after first symptoms 2 days 
Treatment before blood sampling No 
COVID-19 vaccination status prior to MIS-A Unknown 

Pip/Tazo, piperacillin/tazobactam; VA-ECMO, venoarterial extracorporeal membrane oxygenation.

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