Table 1.

Complement profile results for the patient

Result (L, low; H, high)Reference range considered normal
C3 23.4 mg/dl (L) 71–150 mg/dl 
C4 17.7 mg/dl 15.7–47 mg/dl 
C1 esterase inhibitor 19.1 mg/dl (L) 21–39 mg/dl 
C1q 8.9 mg/dl 7.5–20 mg/dl 
C2 4.6 mg/dl (H) 1.9–3.6 mg/dl 
C5 1.7 mg/dl (L) 2.8–6.8 mg/dl 
C6 3.2 mg/dl (L) 4–6.9 mg/dl 
C7 <1.4 mg/dl (L) 3.5–7.9 mg/dl 
C8 2.8 mg/dl (L) 3–5.8 mg/dl 
C9 1.3 mg/dl (L) 2.5–7.5 mg/dl 
Factor B <15 mg/dl (L) 19–50 mg/dl 
FH 8 mg/dl (L) 15.8–37.5 mg/dl 
FI 1.3 mg/dl (L)a 1.6–3.7 mg/dl 
Properdin 7.9 μg/ml (L) 8.1–18.4 μg/ml 
C4-binding protein 43.3% (L) 61–116% 
Result (L, low; H, high)Reference range considered normal
C3 23.4 mg/dl (L) 71–150 mg/dl 
C4 17.7 mg/dl 15.7–47 mg/dl 
C1 esterase inhibitor 19.1 mg/dl (L) 21–39 mg/dl 
C1q 8.9 mg/dl 7.5–20 mg/dl 
C2 4.6 mg/dl (H) 1.9–3.6 mg/dl 
C5 1.7 mg/dl (L) 2.8–6.8 mg/dl 
C6 3.2 mg/dl (L) 4–6.9 mg/dl 
C7 <1.4 mg/dl (L) 3.5–7.9 mg/dl 
C8 2.8 mg/dl (L) 3–5.8 mg/dl 
C9 1.3 mg/dl (L) 2.5–7.5 mg/dl 
Factor B <15 mg/dl (L) 19–50 mg/dl 
FH 8 mg/dl (L) 15.8–37.5 mg/dl 
FI 1.3 mg/dl (L)a 1.6–3.7 mg/dl 
Properdin 7.9 μg/ml (L) 8.1–18.4 μg/ml 
C4-binding protein 43.3% (L) 61–116% 
a

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