| JEM report | Davidson et al., 2024 | Davidson et al., 2024 | Takeda et al., 2024 |
| OTULIN allele | p.C129S | p.C129S | p.R306Q |
| Age | Gestational age at birth | 31 wk | Full-term | 33 wk |
| Disease onset | 4 days | 7 mo | At birth |
| Manifestations | Skin | Necrotizing omphalitis; panniculitis; pathergy | Necrotizing fasciitis; panniculitis | Necrotizing omphalitis; pustulosis |
| Lungs | Acute respiratory distress | Recurrent respiratory tract infections | Acute respiratory distress |
| Laboratory results | Inflammation | Neutrophilia; monocytosis; thrombocytopenia; elevated CRP | Neutrophilia; elevated CRP | Neutrophilia; thrombocytosis; elevated CRP |
| Autoimmunity | Not reported | Absent | Absent |
| Cultures | S. aureus (trace) | Negative | S. aureus (trace) |
| Treatment (response) | Steroids (+); Adalimumab (+); antibiotics (±) | Steroids (+); Infliximab (+); antibiotics (±) | Steroids (+); Etanercept (+); antibiotics (±) |