Table 2.

Experimental results showing the impact of altered mitochondrial Ca2+uptake on cytosolic Ca2+concentration.

ReferenceExperimental
model and
protocol
Cytosolic
transient
amplitude
Cytosolic
transient
duration
Mitochondrial
transient
amplitude
Gillis, 1997  Mechanically skinned fibers
Rhutenium Red 
nd delayed
relaxation
half time +176% 
nd 
Caputo and Bolanos., 2008  FDB fibers
Electrical stimulation
FCCP 2 μM 
decreased −46% no change nd 
Weiss et al., 2010  FDB fibers
Electrical stimulation
FCCP 2.5 μM 
decreased −55% prolonged −37%
(rate constant) 
nd 
Yi et al., 2011  FDB fibers
G93A SOD1 mutation
Voltage clamp 
increased
+15.6% 
no change decreased −14.9% 
Andrade et al., 2005  Intact EO muscles
Electrical stimulation
CCCP 10 μM 
increased +72% nd nd 
Ainbinder et al., 2015  FDB fibers
Electrical stimulation
Mfn2 downregulation 
increased
twitch +10%
Tetanus + 30% 
no change decreased −30% 
Eisner et al., 2014  FDB fibers
Electrical stimulation
Mfn1 KO and downreg 
Increased decay
with repeated
stimulation 
nd decreased uptake 
Mammucari et al., 2015  FDB fibers–caffeine
MCU silencing 
no change nd decreased −45% 
FDB fibers–caffeine
MCU upregulation 
decreased −10% nd increased +76% 
Gherardi et al. 2019  FDB fibers–caffeine
MCU–constitutive KO 
decreased −10% nd decreased to 0 
Favaro et al., 2019  FDB fibers
Electrical stimulation
DRP1-KO
(MCU upregulation) 
decreased −9% nd increased +14.2% 
Debattisti et al., 2019  FDB fibers
Electrical stimulation
MICU1 KO 
trend to decrease no change decreased −30% 
Butera et al., 2021  FDB fibers–caffeine
PVA KO and MCU down
regulation 
increased +36% nd decreased −28% 
ReferenceExperimental
model and
protocol
Cytosolic
transient
amplitude
Cytosolic
transient
duration
Mitochondrial
transient
amplitude
Gillis, 1997  Mechanically skinned fibers
Rhutenium Red 
nd delayed
relaxation
half time +176% 
nd 
Caputo and Bolanos., 2008  FDB fibers
Electrical stimulation
FCCP 2 μM 
decreased −46% no change nd 
Weiss et al., 2010  FDB fibers
Electrical stimulation
FCCP 2.5 μM 
decreased −55% prolonged −37%
(rate constant) 
nd 
Yi et al., 2011  FDB fibers
G93A SOD1 mutation
Voltage clamp 
increased
+15.6% 
no change decreased −14.9% 
Andrade et al., 2005  Intact EO muscles
Electrical stimulation
CCCP 10 μM 
increased +72% nd nd 
Ainbinder et al., 2015  FDB fibers
Electrical stimulation
Mfn2 downregulation 
increased
twitch +10%
Tetanus + 30% 
no change decreased −30% 
Eisner et al., 2014  FDB fibers
Electrical stimulation
Mfn1 KO and downreg 
Increased decay
with repeated
stimulation 
nd decreased uptake 
Mammucari et al., 2015  FDB fibers–caffeine
MCU silencing 
no change nd decreased −45% 
FDB fibers–caffeine
MCU upregulation 
decreased −10% nd increased +76% 
Gherardi et al. 2019  FDB fibers–caffeine
MCU–constitutive KO 
decreased −10% nd decreased to 0 
Favaro et al., 2019  FDB fibers
Electrical stimulation
DRP1-KO
(MCU upregulation) 
decreased −9% nd increased +14.2% 
Debattisti et al., 2019  FDB fibers
Electrical stimulation
MICU1 KO 
trend to decrease no change decreased −30% 
Butera et al., 2021  FDB fibers–caffeine
PVA KO and MCU down
regulation 
increased +36% nd decreased −28% 

The percent variations are in some cases directly reported in the papers and in some cases recalculated from histograms or tables. nd, not determined.

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