Table I.

Impact of the Artemis-P70 mutation on lymphocyte development

Genotype Thymocytes CD4+CD8+ thymocytes Splenocytes CD4+ LN T cells CD8+ LN T cells IgM+ splenocytes Pro–B cells Pro–B cells Pre–B cells Pre–B cells 
 ×106 % ×106 ×106 ×106 % % ×105 % ×105 
Art+/+ (n = 7) 167 ± 102 75 ± 5 70.1 ± 27.95 3.57 ± 2.06 1.72 ± 0.91 19.84 ± 3.82 2.38 ± 0.65 0.71 ± 0.18 15.97 ± 5.69 4.63 ± 1.62 
Art+/P70 (n = 7) 220 ± 106 78 ± 4 94.3 ± 43.2 4.61 ± 2.1 2.1 ± 0.6 18.11 ± 6.2 2.37 ± 0.31 0.897 ± 0.44 10.36 ± 3.25 4.34 ± 4.04 
ArtP70/P70 (n = 6) 19 ± 10 22 ± 15 31.4 ± 19.5 0.43 ± 0.25 0.59 ± 0.2 3.74 ± 1.9 4.44 ± 1.79 1.34 ± 0.56 1.96 ± 0.56 0.75 ± 0.33 
Art−/− (n = 6) 3 ± 2 7 ± 10 15.06 ± 11.4 0.059 ± 0.04 0.02 ± 0.013 0.25 ± 0.21 1.5 ± 1.5 0.55 ± 0.74 0.292 ± 0.23 0.1 ± 0.1 
Genotype Thymocytes CD4+CD8+ thymocytes Splenocytes CD4+ LN T cells CD8+ LN T cells IgM+ splenocytes Pro–B cells Pro–B cells Pre–B cells Pre–B cells 
 ×106 % ×106 ×106 ×106 % % ×105 % ×105 
Art+/+ (n = 7) 167 ± 102 75 ± 5 70.1 ± 27.95 3.57 ± 2.06 1.72 ± 0.91 19.84 ± 3.82 2.38 ± 0.65 0.71 ± 0.18 15.97 ± 5.69 4.63 ± 1.62 
Art+/P70 (n = 7) 220 ± 106 78 ± 4 94.3 ± 43.2 4.61 ± 2.1 2.1 ± 0.6 18.11 ± 6.2 2.37 ± 0.31 0.897 ± 0.44 10.36 ± 3.25 4.34 ± 4.04 
ArtP70/P70 (n = 6) 19 ± 10 22 ± 15 31.4 ± 19.5 0.43 ± 0.25 0.59 ± 0.2 3.74 ± 1.9 4.44 ± 1.79 1.34 ± 0.56 1.96 ± 0.56 0.75 ± 0.33 
Art−/− (n = 6) 3 ± 2 7 ± 10 15.06 ± 11.4 0.059 ± 0.04 0.02 ± 0.013 0.25 ± 0.21 1.5 ± 1.5 0.55 ± 0.74 0.292 ± 0.23 0.1 ± 0.1 

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