Table 1.
Immunological characteristics of patients
P1P2
Age 6 yrAge 26 yrAge 14 yr
Absolute lymphocyte count (×109/liter) 2.4 (1.1–4.5) 1.74 (1.1–4.5) 1.48 (1.1–4.5) 
CD3+ T cells  
 Absolute (×109/liter) 1.7 (0.75–2.51) 1.43 (0.75–2.51) 1.11 (0.75–2.51) 
 % 71 (55–84) 82.3 (55–84) 75 (55–84) 
CD4+ T cells 
 Absolute (×109/liter) 0.94 (0.43–1.69) 0.82 (0.43–1.69) 0.66 (0.43–1.69) 
 % 39 (31–60) 47.1 (31–60) 45 (31–60) 
CD8+ T cells 
 Absolute (×109/liter) 0.67 (0.22–1.21) 0.52 (0.22–1.21) 0.47 (0.22–1.21) 
 % 28 (13–41) 30.1 (13–41) 32 (13–41) 
CD16+/CD56+ NK cells 
 Absolute (×109/liter) 0.12 (0.12–0.60) 0.09 (0.12–0.60) 0.07 (0.12–0.60) 
 % 5 (5–27) 4.9 (5–27) 5 (5–27) 
CD19+ B cells 
 Absolute (×109/liter) 0.48 (0.12–0.64) 0.23 (0.12–0.64) 0.21 (0.12–0.64) 
 % 20 (6–25) 13.3 (6–25) 14 (6–25) 
IgE (KU/liter) 859 (0–48) 7,060 (0–81) 795 (0–81) 
IgG (g/liter) 4.5 (4.9–16.1) 7.71 (6–16) 5.3 (6–16) 
IgG1 (g/liter) 4 (2.3–6.4)   
IgG2 (g/liter) 0.28 (0.4–4.5)   
IgG3 (g/liter) 0.78 (0.1–1.1)   
IgG4 (g/liter) <0.02 (0–0.8)   
IgM (g/liter) 0.5 (0.5–1.9) 0.24 (0.5–1.9) 0.3 (0.5–1.9) 
IgA (g/liter) 0.3 (0.4–2.0) 0.91 (0.8–2.8) 0.6 (0.8–2.8) 
Hib IgG (µg/ml) <0.15 (prevaccine)a 3.01a  
Pneumococcal titer (IU/ml)  38b  
Tetanus IgG (IU/ml) >0.1c   
NBT (%) 0/96  100 
DHR 
 Resting (%)  6 (Control, 2)  
 Stimulated (%)  100 (Control, 100)  
IL-6 (pg/ml)  830.8 (0–7)  
IL-6 (pg/ml)  205.6 (0–7)  
P1P2
Age 6 yrAge 26 yrAge 14 yr
Absolute lymphocyte count (×109/liter) 2.4 (1.1–4.5) 1.74 (1.1–4.5) 1.48 (1.1–4.5) 
CD3+ T cells  
 Absolute (×109/liter) 1.7 (0.75–2.51) 1.43 (0.75–2.51) 1.11 (0.75–2.51) 
 % 71 (55–84) 82.3 (55–84) 75 (55–84) 
CD4+ T cells 
 Absolute (×109/liter) 0.94 (0.43–1.69) 0.82 (0.43–1.69) 0.66 (0.43–1.69) 
 % 39 (31–60) 47.1 (31–60) 45 (31–60) 
CD8+ T cells 
 Absolute (×109/liter) 0.67 (0.22–1.21) 0.52 (0.22–1.21) 0.47 (0.22–1.21) 
 % 28 (13–41) 30.1 (13–41) 32 (13–41) 
CD16+/CD56+ NK cells 
 Absolute (×109/liter) 0.12 (0.12–0.60) 0.09 (0.12–0.60) 0.07 (0.12–0.60) 
 % 5 (5–27) 4.9 (5–27) 5 (5–27) 
CD19+ B cells 
 Absolute (×109/liter) 0.48 (0.12–0.64) 0.23 (0.12–0.64) 0.21 (0.12–0.64) 
 % 20 (6–25) 13.3 (6–25) 14 (6–25) 
IgE (KU/liter) 859 (0–48) 7,060 (0–81) 795 (0–81) 
IgG (g/liter) 4.5 (4.9–16.1) 7.71 (6–16) 5.3 (6–16) 
IgG1 (g/liter) 4 (2.3–6.4)   
IgG2 (g/liter) 0.28 (0.4–4.5)   
IgG3 (g/liter) 0.78 (0.1–1.1)   
IgG4 (g/liter) <0.02 (0–0.8)   
IgM (g/liter) 0.5 (0.5–1.9) 0.24 (0.5–1.9) 0.3 (0.5–1.9) 
IgA (g/liter) 0.3 (0.4–2.0) 0.91 (0.8–2.8) 0.6 (0.8–2.8) 
Hib IgG (µg/ml) <0.15 (prevaccine)a 3.01a  
Pneumococcal titer (IU/ml)  38b  
Tetanus IgG (IU/ml) >0.1c   
NBT (%) 0/96  100 
DHR 
 Resting (%)  6 (Control, 2)  
 Stimulated (%)  100 (Control, 100)  
IL-6 (pg/ml)  830.8 (0–7)  
IL-6 (pg/ml)  205.6 (0–7)  

Abnormal results are shown in bold. Numbers in parentheses indicate reference values of the corresponding measurements. DHR, dihydrorhodamine; Hib, H. influenza bacteria; NBT, nitroblue tetrazolium.

a

Minimum protective level, 0.15 µg/ml; optimum protective level, 1.0 µg/ml.

b

A value of 60 represents the 25th centile of the normal population.

c

Minimum protective level, 0.01 IU/ml; optimum protective level, 0.1 IU/ml; long-term protective level, >1.0 IU/ml.

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