Table 2.
High-resolution CFTR structures to date
ProteinzfCFTRhCFTRzfCFTRhCFTRhCFTRhCFTRchCFTRchCFTR
Orthologue Zebrafish Human Zebrafish Human Human Human Chicken Chicken 
Resolution 3.7 Å 3.9 Å 3.4 Å 3.2 Å 3.3 Å 3.2 Å 4.3 Å 6.6 Å 
Detergent Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (DMNG, digitonin) Detergent (DMNG, digitonin) 
Mutation – – E1372Q E1371Q E1371Q E1371Q ΔRI/1404S/1441X ΔRI/1404S/1441X 
State Closed, inward facing, dephosphorylated, apo-ATP Closed, inward facing, dephosphorylated, apo-ATP Closed, outward facing, phosphorylated, ATP-bound Closed, outward facing, Phosphorylated, ATP-bound Closed, outward facing, Phosphorylated, ATP-bound, VX-770-bound Closed, outward facing, Phosphorylated, ATP-bound, GLPG1837-bound Closed, inward facing, dephosphorylated, ATP-present Closed, inward facing, phosphorylated, ATP-present 
PDB accession no. 5UAR 5UAK 5W81 6MSM 6O2P 6O1V 6D3R 6D3S 
Year 2016 2017 2017 2018 2019 2019 2018 2018 
ProteinzfCFTRhCFTRzfCFTRhCFTRhCFTRhCFTRchCFTRchCFTR
Orthologue Zebrafish Human Zebrafish Human Human Human Chicken Chicken 
Resolution 3.7 Å 3.9 Å 3.4 Å 3.2 Å 3.3 Å 3.2 Å 4.3 Å 6.6 Å 
Detergent Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (LMNG, digitonin, CHS) Detergent (DMNG, digitonin) Detergent (DMNG, digitonin) 
Mutation – – E1372Q E1371Q E1371Q E1371Q ΔRI/1404S/1441X ΔRI/1404S/1441X 
State Closed, inward facing, dephosphorylated, apo-ATP Closed, inward facing, dephosphorylated, apo-ATP Closed, outward facing, phosphorylated, ATP-bound Closed, outward facing, Phosphorylated, ATP-bound Closed, outward facing, Phosphorylated, ATP-bound, VX-770-bound Closed, outward facing, Phosphorylated, ATP-bound, GLPG1837-bound Closed, inward facing, dephosphorylated, ATP-present Closed, inward facing, phosphorylated, ATP-present 
PDB accession no. 5UAR 5UAK 5W81 6MSM 6O2P 6O1V 6D3R 6D3S 
Year 2016 2017 2017 2018 2019 2019 2018 2018 

ch, chicken; CHS, cholesteryl hemisuccinate; DMNG, decyl maltose neopentyl glycol; LMNG, lauryl maltose neopentyl glycol; zf, zebrafish.

or Create an Account

Close Modal
Close Modal