Table 2.
Mechanical and energetic parameters of permeabilized ventricular strips from the homozygous K280N cTnT HCM patient and three groups of control patients
K280N (N = 1, n = 16)Donors (N = 2, n = 12)LVHao (N = 3, n = 13)HCMsmn (N = 6, n = 29)
Maximal tension (kN m−2) 13.5 ± 1.8* 38.7 ± 1.2 21.3 ± 1.5 25.6 ± 1.6 
Maximal ATPase activity (μmol L−1 s−1) 38.4 ± 4.8 91.0 ± 4.7 52.2 ± 6.3 45.2 ± 2.7 
Tension cost (μmol L−1 s−1/ kN m−2) 3.1 ± 0.3* 2.3 ± 0.1 2.5 ± 0.3 1.8 ± 0.1 
Basal ATPase activity (μmol L−1 s−1) 4.6 ± 0.8 10.9 ± 2.1 10.3 ± 2.2 7.2 ± 1.0 
K280N (N = 1, n = 16)Donors (N = 2, n = 12)LVHao (N = 3, n = 13)HCMsmn (N = 6, n = 29)
Maximal tension (kN m−2) 13.5 ± 1.8* 38.7 ± 1.2 21.3 ± 1.5 25.6 ± 1.6 
Maximal ATPase activity (μmol L−1 s−1) 38.4 ± 4.8 91.0 ± 4.7 52.2 ± 6.3 45.2 ± 2.7 
Tension cost (μmol L−1 s−1/ kN m−2) 3.1 ± 0.3* 2.3 ± 0.1 2.5 ± 0.3 1.8 ± 0.1 
Basal ATPase activity (μmol L−1 s−1) 4.6 ± 0.8 10.9 ± 2.1 10.3 ± 2.2 7.2 ± 1.0 

Means ± SE; N, number of patients in the group; n, number of muscle strips. For the statistics of the comparison between groups, see Supplemental materials; *, K280N parameters for which the statistical analysis shows a significant difference versus control groups.

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