Table I.

Changes in the sensitivity of RYR2 to be opened by [Ca2+]i

A—Increase in RYR2 sensitivity B—Decrease in RYR2 sensitivity 
Increased [Ca2+]SR Decreased [Ca2+]SR 
 (Lukyanenko et al., 1996; Györke and Györke, 1998; Györke et al., 2002)  (Lukyanenko et al., 1996; Györke and Györke, 1998; Györke et al., 2002) 
RYR2 phosphorylation at PKA or CaMKII sites Calstabin2 (FKBP 12.6) binding 
 (Valdivia et al., 1995; Li et al., 1998; Marx et al., 2000)  (Marx et al., 2000; Wehrens et al., 2003) 
Caffeine Tetracaine 
 (Rousseau and Meissner, 1989; O’Neill and Eisner, 1990; Venetucci et al., 2007)  (Xu et al., 1993; Overend et al., 1997) 
RYR2 oxidation (ROS) Anti-oxidation 
 (Hidalgo et al., 2002; Terentyev et al., 2008)  (Hidalgo et al., 2002; Terentyev et al., 2008) 
RYR2 CPVT mutations  
 (Marks et al., 2002; Wehrens et al., 2003)  
Calsequestrin mutations  
 (Postma et al., 2002; Eldar et al., 2003; di Barletta et al., 2006; Knollmann et al., 2006)  
Triadin  
 (Valdivia et al., 1995; Li et al., 1998; Marx et al., 2000; Györke and Terentyev, 2008; Chopra et al., 2009)  
RYR2 nitrosylation  
 (Xu et al., 1998; Sun et al., 2008; Bellinger et al., 2009)  
A—Increase in RYR2 sensitivity B—Decrease in RYR2 sensitivity 
Increased [Ca2+]SR Decreased [Ca2+]SR 
 (Lukyanenko et al., 1996; Györke and Györke, 1998; Györke et al., 2002)  (Lukyanenko et al., 1996; Györke and Györke, 1998; Györke et al., 2002) 
RYR2 phosphorylation at PKA or CaMKII sites Calstabin2 (FKBP 12.6) binding 
 (Valdivia et al., 1995; Li et al., 1998; Marx et al., 2000)  (Marx et al., 2000; Wehrens et al., 2003) 
Caffeine Tetracaine 
 (Rousseau and Meissner, 1989; O’Neill and Eisner, 1990; Venetucci et al., 2007)  (Xu et al., 1993; Overend et al., 1997) 
RYR2 oxidation (ROS) Anti-oxidation 
 (Hidalgo et al., 2002; Terentyev et al., 2008)  (Hidalgo et al., 2002; Terentyev et al., 2008) 
RYR2 CPVT mutations  
 (Marks et al., 2002; Wehrens et al., 2003)  
Calsequestrin mutations  
 (Postma et al., 2002; Eldar et al., 2003; di Barletta et al., 2006; Knollmann et al., 2006)  
Triadin  
 (Valdivia et al., 1995; Li et al., 1998; Marx et al., 2000; Györke and Terentyev, 2008; Chopra et al., 2009)  
RYR2 nitrosylation  
 (Xu et al., 1998; Sun et al., 2008; Bellinger et al., 2009)  

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