Table 1.

Hemograms for USP18-deficient patients

ComponentP1Normal rangeP2Normal range
Red cells (× 109/liter) 4.5 4.5–4.9 3.89 3.9–4.6 
Hemoglobin (g/dl) 11.9 13–14.5 9.30 11.5–12 
Hematocrit (%) 35 37–43 29.40 34–37 
VGM (fl) 79.7 78–88 75.60 75–81 
Leucocytes (× 109/liter) 4.1 4.5–13.5 5.0 6–17 
Neutrophils (× 109/liter) 1.0 1.8–8.0 2.90 1.5–8.5 
Eosinophils (× 109/liter) 0.4 0–0.3 0–0.3 
Basophils (× 109/liter) 0–0.2 0–0.2 
Lymphocytes (× 109/liter) 2.1 1.2–5.2 1.40 2–8 
Monocytes (× 109/liter) 0.6 0.2–1 0.60 0.2–1 
Platelets (× 109/liter) 212 150–450 344 175–200 
ComponentP1Normal rangeP2Normal range
Red cells (× 109/liter) 4.5 4.5–4.9 3.89 3.9–4.6 
Hemoglobin (g/dl) 11.9 13–14.5 9.30 11.5–12 
Hematocrit (%) 35 37–43 29.40 34–37 
VGM (fl) 79.7 78–88 75.60 75–81 
Leucocytes (× 109/liter) 4.1 4.5–13.5 5.0 6–17 
Neutrophils (× 109/liter) 1.0 1.8–8.0 2.90 1.5–8.5 
Eosinophils (× 109/liter) 0.4 0–0.3 0–0.3 
Basophils (× 109/liter) 0–0.2 0–0.2 
Lymphocytes (× 109/liter) 2.1 1.2–5.2 1.40 2–8 
Monocytes (× 109/liter) 0.6 0.2–1 0.60 0.2–1 
Platelets (× 109/liter) 212 150–450 344 175–200 

VGM, average globular volume.

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