Table 1.
Clinical phenotype of patients
Patient, origin, gender, present age (yr)Infectious diseasesCutaneous featuresOthersLevel of IgE
    KIU/ml 
A1     
Morocco Purulent otitis Scaly erythroderma Bronchitis <5 
Male Multifocal tuberculosis Focal alopecia Peptic stenosis of the esophagus  
Died at 17 Onychomycosis with perionyxis Pustular-like and scaly lesions on the soles   
 CMC (perionyxis)    
A2     
Morocco CMC (perionyxis and oral thrush) Scaly erythroderma Bilateral bronchoalveolar syndrome <2 
Female Recurrent bacterial lung infections    
    
A3     
Morocco CMC (perionyxis) Scaly erythroderma Recurrent bacterial lung infections <2 
Female Bilateral bronchoalveolar syndrome    
    
B1     
Tunisia Recurrent purulent otitis Eczema Bronchial dilatation 1,381 
Female Subcutaneous abscesses Cold urticaria Asthma  
27 Molluscum contagiosum Lupus-like facial erythema Allergy to yolk egg and peanut  
 Recurrent bacterial lung infections Hyperpigmented lesions   
 Gastritis by Helicobacter pylori    
B2     
Tunisia Pneumonia Eczema Recurrent bronchopneumonia 2.3 
Female  Psoriasis guttata-like lesions Bronchial dilatation  
26 Subcutaneous abscesses Mild ichthyosis Asthma  
  Sun intolerance   
 Molluscum contagiosum Dry skin   
  Large inflammatory and erosive inverted psoriasis-like plaques in the folds   
C1     
Turkey Miliary tuberculosis Seborrheic dermatitis Asthma 34.7 
Male     
19     
Patient, origin, gender, present age (yr)Infectious diseasesCutaneous featuresOthersLevel of IgE
    KIU/ml 
A1     
Morocco Purulent otitis Scaly erythroderma Bronchitis <5 
Male Multifocal tuberculosis Focal alopecia Peptic stenosis of the esophagus  
Died at 17 Onychomycosis with perionyxis Pustular-like and scaly lesions on the soles   
 CMC (perionyxis)    
A2     
Morocco CMC (perionyxis and oral thrush) Scaly erythroderma Bilateral bronchoalveolar syndrome <2 
Female Recurrent bacterial lung infections    
    
A3     
Morocco CMC (perionyxis) Scaly erythroderma Recurrent bacterial lung infections <2 
Female Bilateral bronchoalveolar syndrome    
    
B1     
Tunisia Recurrent purulent otitis Eczema Bronchial dilatation 1,381 
Female Subcutaneous abscesses Cold urticaria Asthma  
27 Molluscum contagiosum Lupus-like facial erythema Allergy to yolk egg and peanut  
 Recurrent bacterial lung infections Hyperpigmented lesions   
 Gastritis by Helicobacter pylori    
B2     
Tunisia Pneumonia Eczema Recurrent bronchopneumonia 2.3 
Female  Psoriasis guttata-like lesions Bronchial dilatation  
26 Subcutaneous abscesses Mild ichthyosis Asthma  
  Sun intolerance   
 Molluscum contagiosum Dry skin   
  Large inflammatory and erosive inverted psoriasis-like plaques in the folds   
C1     
Turkey Miliary tuberculosis Seborrheic dermatitis Asthma 34.7 
Male     
19     

CMC, chronic mucocutaneous candidiasis.

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