Table I.

Genomic instability in WASP-I296T B and T cells

 Metaphases Chromosome breaks >40 chromosomes per metaphase >40 chromosomes per nucleus Other 
B cells      
WT WASP 51 
 131 
 79 
WASP KO 81 
 71 
 54 
WASP-I296T 160 16 1 fused chromosome 
 73 2 doublet chromosomes 
 56 
T cells      
WT WASP 50 
 38 
 72 1 doublet chromosome 
WASP-I296T 39 
 206 17 1 doublet chromosome 
 64 1 doublet chromosome 
 Metaphases Chromosome breaks >40 chromosomes per metaphase >40 chromosomes per nucleus Other 
B cells      
WT WASP 51 
 131 
 79 
WASP KO 81 
 71 
 54 
WASP-I296T 160 16 1 fused chromosome 
 73 2 doublet chromosomes 
 56 
T cells      
WT WASP 50 
 38 
 72 1 doublet chromosome 
WASP-I296T 39 
 206 17 1 doublet chromosome 
 64 1 doublet chromosome 

Quantification of chromosomal aberrations in B and T cells. Each row represents an analysis of cells from one mouse. It was not possible to assess genomic instability in WASP-deficient T cells because they fail to proliferate in response to receptor activation.

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