Table 2.
Examples of mouse models underscoring telomere dysfunction as either a driving force in cancer development or as a cancer suppressor
GenotypeCancer phenotypeReference
Terc−/− p53−/−       Earlier onset lymphoma/sarcoma, epithelial carcinoma Chin et al., 1999  
Terc−/− Msh2−/−       Lymphoma/carcinoma Martinez et al., 2009a  
Trf1lox/lox K5-cre p53−/−       Squamous cell carcinoma Martínez et al., 2009b  
Pot1alox/lox p53lox/lox hCD2-iCre       T cell lymphomas Pinzaru et al., 2016  
Pot1alox/lox p53lox/lox Sprr2f-Cre       Endometrial adenocarcinomas Akbay et al., 2013  
Tpp1Acd p53−/−       Carcinomas Else et al., 2009  
Tpp1lox/lox K5-cre p53−/−       Cancer suppressor Tejera et al., 2010  
Terc−/− Ink4a/Arf−/−       Delayed lymphoma/fibrosarcoma onset Khoo et al., 2007  
Trf1lox/lox p53−/− K-RasLSLG12V       Growth impairment of lung carcinoma García-Beccaria et al., 2015  
GenotypeCancer phenotypeReference
Terc−/− p53−/−       Earlier onset lymphoma/sarcoma, epithelial carcinoma Chin et al., 1999  
Terc−/− Msh2−/−       Lymphoma/carcinoma Martinez et al., 2009a  
Trf1lox/lox K5-cre p53−/−       Squamous cell carcinoma Martínez et al., 2009b  
Pot1alox/lox p53lox/lox hCD2-iCre       T cell lymphomas Pinzaru et al., 2016  
Pot1alox/lox p53lox/lox Sprr2f-Cre       Endometrial adenocarcinomas Akbay et al., 2013  
Tpp1Acd p53−/−       Carcinomas Else et al., 2009  
Tpp1lox/lox K5-cre p53−/−       Cancer suppressor Tejera et al., 2010  
Terc−/− Ink4a/Arf−/−       Delayed lymphoma/fibrosarcoma onset Khoo et al., 2007  
Trf1lox/lox p53−/− K-RasLSLG12V       Growth impairment of lung carcinoma García-Beccaria et al., 2015  

The effects of telomere dysfunction in cancer-prone mouse models depend on the status of DNA damage surveillance mechanisms, acting oncogenes, and tissue-specific factors.

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