Table 2.
The characterization of the CMT2A mutation
Mutated genePositionAmino acid changeZygosityInheritance1000 Genomes Minor Allele Frequency
Confirmed mutation KIF1B CHR1: 10387567 Y1087C Heterozygote Autosomal dominant 0.0395 
Analyzed genes AARS (601065), ATL1 (606439), DNM2 (602378), DNMT1 (126375), DYNC1H1 (600112), EGR2 (129010), FGD4 (611104), GARS (600287), GDAP1 (606598), GJB1 (304040), GLA (300644), HSPB1 (602195), HSPB8 (608014), KIF1B (605995), LITAF (603795), LMNA (150330), LRSAM1 (610933), MED25 (610197), MFN2 (608507), MPZ (159440), MTMR2 (603557), NDRG1 (605262), NEFL (162280), PMP22 (601097), PRX (605725), RAB7A (602298), SBF2 (607697), SCN9A (603415), SH3TC2 (608206), SPTLC2 (605713), TRPV4 (605427), TTR (176300), and YARS (603623) 
Mutated genePositionAmino acid changeZygosityInheritance1000 Genomes Minor Allele Frequency
Confirmed mutation KIF1B CHR1: 10387567 Y1087C Heterozygote Autosomal dominant 0.0395 
Analyzed genes AARS (601065), ATL1 (606439), DNM2 (602378), DNMT1 (126375), DYNC1H1 (600112), EGR2 (129010), FGD4 (611104), GARS (600287), GDAP1 (606598), GJB1 (304040), GLA (300644), HSPB1 (602195), HSPB8 (608014), KIF1B (605995), LITAF (603795), LMNA (150330), LRSAM1 (610933), MED25 (610197), MFN2 (608507), MPZ (159440), MTMR2 (603557), NDRG1 (605262), NEFL (162280), PMP22 (601097), PRX (605725), RAB7A (602298), SBF2 (607697), SCN9A (603415), SH3TC2 (608206), SPTLC2 (605713), TRPV4 (605427), TTR (176300), and YARS (603623) 

or Create an Account

Close Modal
Close Modal