Table 1.

Candidate genes and complexes in telomere disorders

Genes that cause telomere disorders when defective Process/complex Diseases Process/complex including genes that cause telomeropathies Candidate genes 
TIN2 Shelterin, inhibits TRF1 PARsylation DKC/HHS/Revesz syndrome Shelterin TRF1, TRF2, TIN2, RAP1, TPP1, POT1 
RTEL1 T-loop dissociation, target of cytosolic iron–sulfur protein assembly (CIA) complex DKC/HHS CST complex CTC1, STN1, TEN1 
CTC1 CST complex Coats Plus Telomerase TERT, TERC, Dyskerin, NHP2, NOP10, GAR1 
Apollo Overhang processing HHS CIA complex MMS19, MIP18, CIAO1, IOP1, RTEL1 
TERT, TERC, Dyskerin, NHP2, NOP10 Telomerase IPF, DKC, aplastic anemia Apollo TRF2, FANCD2, Apollo 
TCAB1 Cajal body, telomerase assembly DKC Cajal body Coilin, HOT1, TCAB1, Telomerase complex 
   TRF1 regulation TRF1, TNKS1, TIN2, TNKS1BP1 
Genes that cause telomere disorders when defective Process/complex Diseases Process/complex including genes that cause telomeropathies Candidate genes 
TIN2 Shelterin, inhibits TRF1 PARsylation DKC/HHS/Revesz syndrome Shelterin TRF1, TRF2, TIN2, RAP1, TPP1, POT1 
RTEL1 T-loop dissociation, target of cytosolic iron–sulfur protein assembly (CIA) complex DKC/HHS CST complex CTC1, STN1, TEN1 
CTC1 CST complex Coats Plus Telomerase TERT, TERC, Dyskerin, NHP2, NOP10, GAR1 
Apollo Overhang processing HHS CIA complex MMS19, MIP18, CIAO1, IOP1, RTEL1 
TERT, TERC, Dyskerin, NHP2, NOP10 Telomerase IPF, DKC, aplastic anemia Apollo TRF2, FANCD2, Apollo 
TCAB1 Cajal body, telomerase assembly DKC Cajal body Coilin, HOT1, TCAB1, Telomerase complex 
   TRF1 regulation TRF1, TNKS1, TIN2, TNKS1BP1 

All genes known to cause telomeropathies when defective are listed, as well as the telomere/telomerase-relevant complexes they participate in. Bold indicates a gene known to cause telomeropathies; genes listed without bold are putative candidate genes due to their known interactions. References for complexes not already discussed in the text: CIA complex (Seki et al., 2013), Cajal body proteins (Kappei et al., 2013), and TRF1 regulation (Seimiya and Smith, 2002; Ye and de Lange, 2004). PARsylation, poly(ADP-ribosyl)ation.

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